Etiologies
Infiltrative diseases
Sarcoidosis (non-reversible, tx w/steroids)
Amyloidosis
Scleroderma (non-reversible, tx w/steroids)
Storage diseases
Hemochromotosis (reversible!)
Endomyocardial fibrosis
Idiopathic
Sx
Diastolic dysfunction
Signs of right-sided heart failure
Prominent JVD
Bilateral ankle edema
Tender hepatomegaly
Signs of left-sided heart failure can be seen
Bibasilar rales
Pleural effusion
Left ventricular volume is normal
Symmetric thickening of the ventricle helps to differentiate restrictive from hypertrophic cardiomyopathy, in which the interventriclar septum is thickest